Understanding Congenital Heart Defects

May 15, 2025

Congenital Heart Defects: Obstructed and Mixed Blood Flow

Introduction

  • Presenter: Cathy from Level Up RN
  • Focus: Congenital heart defects causing obstructed and mixed blood flow
  • Includes a quiz to test knowledge

Obstructed Blood Flow Defects

Coarctation of the Aorta

  • Description: Narrowing of the aorta
  • Implications: Upper extremities receive adequate blood; lower extremities do not
  • Signs & Symptoms:
    • Upper extremity hypertension
    • Bounding pulses in upper extremities
    • Weak pulses, cool skin, and pallor in lower extremities
  • Treatment:
    • Balloon angioplasty or stents
    • Surgical removal of narrowed section
    • Hypertension management with medications

Aortic Stenosis

  • Description: Narrowing of the aortic valve
  • Implications: Decreased blood flow to the whole body
  • Signs & Symptoms:
    • Hypotension
    • Decreased pulses
    • Tachycardia
    • Poor feeding and exercise intolerance
  • Treatment:
    • Balloon dilation or valvotomy

Pulmonary Stenosis

  • Description: Narrowing of the pulmonary valve
  • Implications: Obstructs blood flow to the lungs
  • Signs & Symptoms:
    • Systolic ejection murmur
    • Cyanosis
    • Cardiomegaly
    • Heart failure
  • Treatment:
    • Balloon dilation or valvotomy

Mixed Blood Flow Defects

Transposition of the Great Arteries (TGA)

  • Description: Reversed connections of the aorta and pulmonary artery
  • Implications: Deoxygenated blood pumped to body; oxygenated blood cycled back to lungs
  • Signs & Symptoms:
    • Heart failure
    • Shortness of breath
    • Cardiomegaly
    • Cyanosis, hypoxia, murmurs
    • Fatigue and poor growth
  • Treatment:
    • Prostaglandins to maintain patent ductus arteriosus (PDA)
    • Surgery within the first week of life

Total Anomalous Pulmonary Venous Connection (TAPVC)

  • Description: Pulmonary veins connect to right side of heart
  • Implications: Oxygenated blood returns to lungs
  • Signs & Symptoms:
    • Cyanosis
    • Dyspnea
    • Poor feeding
  • Treatment:
    • Surgical repair to correct vein connections

Truncus Arteriosus

  • Description: Single vessel instead of separate pulmonary artery and aorta
  • Implications: Mixing of blood due to VSD (Ventricular Septal Defect)
  • Signs & Symptoms:
    • Heart failure
    • Murmurs
    • Cyanosis
    • Poor feeding
  • Treatment:
    • Surgical repair within first few months

Hypoplastic Left Heart Syndrome

  • Description: Underdevelopment of the left side of the heart
  • Implications: Inadequate systemic circulation
  • Signs & Symptoms:
    • Cyanosis
    • Heart failure
    • Cold extremities
    • Lethargy
  • Treatment:
    • Prostaglandins to maintain PDA
    • Three-stage surgery: Norwood procedure, Glenn shunt, Fontan procedure

Quiz Questions

  1. Murmur with Pulmonary Stenosis: Systolic ejection murmur
  2. Defect with Upper Extremity Hypertension: Coarctation of the aorta
  3. Reversed Arterial Connections: Transposition of the great arteries

Closing Remarks

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